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Case Report

Lung Transplantation as a Viable Option of Treatment for Pulmonary Veno-Occlusive Disease

by
Marek Ochman
,
Maciej Urlik
,
Zofia Tatoj
,
Marta Wajda-Pokrontka
,
Fryderyk Zawadzki
,
Magdalena Latos
* and
Marian Zembala
Department of Cardiac, Vascular and Endovascular Surgery and Transplantology, SDMZ in Zabrze, Medical University of Silesia in Katowice, Silesian Centre for Heart Disease in Zabrze, Zabrze, Poland
*
Author to whom correspondence should be addressed.
Adv. Respir. Med. 2018, 86(5), 249-254; https://doi.org/10.5603/ARM.2018.0040
Submission received: 9 July 2018 / Revised: 8 October 2018 / Accepted: 8 October 2018 / Published: 30 October 2018

Abstract

Pulmonary veno-occlusive disease (PVOD) is a rare form of pulmonary hypertension caused by alteration of pulmonary veins. Many clinical and hemodynamic similarities to idiopathic pulmonary arterial hypertension (IPAH) may cause diagnostic and therapeutic difficulties. This case report is about a patient with PVOD, whose first symptoms of the disease occurred after infectious mononucleosis. The patient was administered prostacycline (PGI2) mimetic (Treprostinil), which made qualification process and lung transplantation possible. Despite more and more knowledge about the causes, ethiopathogenesis and changes in pulmonary veins on molecular level, lung transplantation is the only successful therapeutic option for patients suffering from PVOD.
Keywords: pulmonary veno-occlusive disease; lung transplantation; idiopathic pulmonary arterial hypertension pulmonary veno-occlusive disease; lung transplantation; idiopathic pulmonary arterial hypertension

Share and Cite

MDPI and ACS Style

Ochman, M.; Urlik, M.; Tatoj, Z.; Wajda-Pokrontka, M.; Zawadzki, F.; Latos, M.; Zembala, M. Lung Transplantation as a Viable Option of Treatment for Pulmonary Veno-Occlusive Disease. Adv. Respir. Med. 2018, 86, 249-254. https://doi.org/10.5603/ARM.2018.0040

AMA Style

Ochman M, Urlik M, Tatoj Z, Wajda-Pokrontka M, Zawadzki F, Latos M, Zembala M. Lung Transplantation as a Viable Option of Treatment for Pulmonary Veno-Occlusive Disease. Advances in Respiratory Medicine. 2018; 86(5):249-254. https://doi.org/10.5603/ARM.2018.0040

Chicago/Turabian Style

Ochman, Marek, Maciej Urlik, Zofia Tatoj, Marta Wajda-Pokrontka, Fryderyk Zawadzki, Magdalena Latos, and Marian Zembala. 2018. "Lung Transplantation as a Viable Option of Treatment for Pulmonary Veno-Occlusive Disease" Advances in Respiratory Medicine 86, no. 5: 249-254. https://doi.org/10.5603/ARM.2018.0040

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