Association between Oral Health-Related Quality of Life in People with Rare Diseases and Their Satisfaction with Dental Care in the Health System of the Federal Republic of Germany
Abstract
:1. Introduction
2. Methods
2.1. Study Design
2.2. Participants
2.3. Data Source
2.4. Statistical Analysis
3. Results
3.1. Participants
3.2. Descriptive Data
3.3. Statistical Analysis
4. Discussion
4.1. Limitations
4.2. Interpretation
5. Conclusions
Supplementary Materials
Author Contributions
Funding
Acknowledgments
Conflicts of Interest
References
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Name of Disease | OMIM Number | Number of Individuals | Mean OHIP Value | Satisfied with Dentist | Satisfied with Health System |
---|---|---|---|---|---|
Marfan syndrome | 154700 | 51 | 13.10 | 90.00% | 44.44% |
Ectodermal dysplasia | 305100 | 46 | 15.32 | 97.61% | 15.56% |
Achalasia | 231550 | 44 | 8.72 | 95.12% | 51.28% |
Sarcoidosis | 181000 | 36 | 13.11 | 97.61% | 51.63% |
Ehlers–Danlos syndrome | 120180 | 32 | 18.90 | 76.77% | 27.03% |
Lymphangioleiomyomatosis | 606690 | 17 | 6.35 | 100% | 53.33% |
Alpha-1-Antitrypsin deficiency | 613490 | 15 | 5.40 | 93.33% | 60.00% |
Syringomyelia | 118420 | 13 | 20.91 | 90.91% | 14.29% |
X-linked hypophosphatemia | 307800 | 13 | 13.85 | 83.33% | 23.07% |
Fabry disease | 301500 | 8 | 7.38 | 100% | 42.86% |
Tuberous sclerosis | 191100 613254 | 7 | 12.86 | 100% | 16.67% |
Von Willebrand disease | 193400 277480 314560 613554 | 7 | 6.00 | 100% | 100% |
Lupus erythematosus | 614420 | 6 | 15.17 | 100% | 100% |
Spinocerebellar ataxia | 164400 | 6 | 11.33 | 100% | 66.67% |
Poliomyelitis | N/A | 5 | 4.00 | 100% | 60.00% |
Prader–Willi syndrome | 176270 | 5 | 6.60 | 60.00% | 60.00% |
Systemic sclerosis | 181750 | 5 | 36.00 | 100% | 25.00% |
Satisfaction with the Dentist | |||||
Sex | Dissatisfied | Satisfied | Total | X2-Test | p-Value |
Male | 10 | 145 | 155 | 0.312 | 0.577 |
Female | 24 | 280 | 304 | ||
Total | 34 | 425 | 459 | ||
Satisfaction with the public system | |||||
Sex | Dissatisfied | Satisfied | Total | X2-Test | p-Value |
Male | 93 | 67 | 160 | 0.335 | 0.563 |
Female | 152 | 123 | 275 | ||
Total | 245 | 190 | 435 | ||
Satisfaction with the public system | Satisfaction with the dentist | ||||
Dissatisfied | Satisfied | Total | X2-Test | p-Value | |
Dissatisfied | 24 | 201 | 225 | 5.818 | 0.016 |
Satisfied | 8 | 179 | 187 | ||
Total | 32 | 380 | 412 | ||
Difficulties in finding a dentist | Satisfaction with the dentist | ||||
Dissatisfied | Satisfied | Total | X2-Test | p-Value | |
No | 22 | 325 | 347 | 4.838 | 0.028 |
Yes | 11 | 70 | 81 | ||
Total | 33 | 395 | 428 |
n | OHIP Values | τ | p-Value | |
---|---|---|---|---|
Age | 480 | 0.009 | 0.392 | |
Travel time | 480 | 0.132 * | 0.000 | |
Sex | 480 | Male: 11.60 ± 12.10 | 0.081 * | 0.018 |
Female: 13.59 ± 12.91 | ||||
Difficulties in finding dentist | 448 | Yes: 23.05 ± 15.01 | 0.293 | 0.00 |
No: 10.86 ± 11.28 | ||||
Satisfaction with Dentist | 452 | Dissatisfied: 23.38 ± 16.52 | −0.157 * | 0.000 |
Satisfied: 12.56 ± 12.45 | ||||
Satisfaction with the System | 428 | Dissatisfied:16.07 ± 13.43 | −0.242 * | 0.000 |
Satisfied: 8.54 ± 10.45 |
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Hanisch, M.; Wiemann, S.; Bohner, L.; Kleinheinz, J.; Jung, S. Association between Oral Health-Related Quality of Life in People with Rare Diseases and Their Satisfaction with Dental Care in the Health System of the Federal Republic of Germany. Int. J. Environ. Res. Public Health 2018, 15, 1732. https://doi.org/10.3390/ijerph15081732
Hanisch M, Wiemann S, Bohner L, Kleinheinz J, Jung S. Association between Oral Health-Related Quality of Life in People with Rare Diseases and Their Satisfaction with Dental Care in the Health System of the Federal Republic of Germany. International Journal of Environmental Research and Public Health. 2018; 15(8):1732. https://doi.org/10.3390/ijerph15081732
Chicago/Turabian StyleHanisch, Marcel, Sabrina Wiemann, Lauren Bohner, Johannes Kleinheinz, and Susanne Jung. 2018. "Association between Oral Health-Related Quality of Life in People with Rare Diseases and Their Satisfaction with Dental Care in the Health System of the Federal Republic of Germany" International Journal of Environmental Research and Public Health 15, no. 8: 1732. https://doi.org/10.3390/ijerph15081732